Food Processing, Second Edition provides incisive coverage of the growth, economic development, and business management of the U.S. commercial food processing industry. This revised edition addresses the many important changes that have affected the industry in the last decade, from new technologies and international trade agreements to the influx of foreign investment and the development of emerging markets around the world. Providing a full-scale analysis of the forces that will shape competitive advantage into the next century, this book is essential reading for food processing managers, buyers, marketers, and their professional advisers. The new volume contains:
* A systematic examination of industrial structure, business organization, and geographic location.
* A discussion of the impact of new processing and information technologies, developments in biotechnology, and more.
* Expanded material on distribution channels and sourcing options, including new retail formats such as warehouse stores and supercenters.
* Information on key input utilization, procurement, product and promotion strategies.
* Predicted growth trends for domestic and foreign markets, the dynamics of industry globalization, and more.

With improved control of most environmental causes of disease, genetic illness has assumed a primary importance in the causation of handicap and mortality in all age groups. At present, effective therapy is available for relatively few genetic conditions and prenatal diagnosis is an important option for couples at high risk. The task of providing prenatal diagnosis for these couples requires a team approach between clinicians and scientists, and is complicated by the large number of diverse conditions and by the rapid developments in the field, both obstetric in relation to imaging and tissue sampling methods and genetic in relation to techniques for analysis. Against this background, the aim of the Symposium was to provide an overview of the current status of prenatal and perinatal diagnosis of inborn errors of metabolism. The format consisted of the usual mixture of specific invited overviews and free communications in either oral or poster form. The invited overviews, as can be seen from this publication, covered a wide range, from accepted methods for neonatal diagnosis and screening to newer techniques for prenatal diagnosis and likely future developments with respect to gene therapy. Similarly, the oral com munications included reviews of experience with biochemical analysis of chorionic villus sampling from major centres, more specific examples of progress towards the basic defect in Batten's disease and Canavan's disease, and prospects for effective therapy in Menkes' disease and a lipid myopathy."

Das in letzter Zeit rapide gewachsene Wissen urn genetische Ursachen von Gesundheit und Krankheit blieb nicht ohne Auswirkungen auf Wissenschaft und Klinik (Tabelle 1.2). Das Studium seltener genetischer St6rungen fiihrte zu besserem Verstandnis der normalen Physiologie: Ein GroBteil unserer heutigen Kenntnis von Stoffwechselwegen beruht auf diesen Forschungen. Entsprechend ist zu vermuten, daB durch Untersuchungen von angeborenen MiBbil dungen und gene tisch bedingtem Krebs unser Verstandnis fur Gewebeentwicklung und -differenzierung wachsen wird. Betroffenen Familien kann durch verbesserte genetische Beratung und zunehmende M6g1ichkeiten in Therapie und Pravention geholfen werden. Fur die Zukunft ist Fortschritt nicht nur hier, sondern auch bei pranatalem und prakonzeptionellem Screening und im Bereich der Pravention zu erwarten. Dies durfte zu einer Reduktion genetisch bedingter Erkrankungen fiihren, zum Nutzen der betroffenen Familien ebenso wie der Gesellschaft im ganzen. Weiterfiihrende Literatur Cori GT, Cori CF (1952) Glucose-6-phosphatase of liver in glycogen storage disease. J Bioi Chern 199:661-667 Donahue RP, Bias WB, Renwick JH, McKusick VA (1968) Probable assignment of the Duffy blood group locus to chromosome 1 in man. Proc Natl Acad Sci USA 6:949-955 Garrod AE (1902) The incidence of alkaptonuria: a study in chemical individuality. Lancat 2: 1616-1620 Ingram VM (1956) A specific chemical difference between the globins of normal human and sickle cell anaema haemoglobin. Nature 178:792-794 Lejeune J, Gautier M, Turpin R (1959) Etude des chromosomes somatiques de neuf infants mongoliens."