Cystic fibrosis is the most common life-threatening inherited disease in the UK and Europe. It affects around 1 in 2500 live births in the UK. There have been enormous advances in the treatment of CF over the last 40 years, with life expectancy increasing from just 5 years in 1964 to mid 30s today, and it now affects as many adults as children. The burden of care for CF patients is, however, considerable, and with the increase in life expectancy the impact of CF on respiratory medicine has increased considerably.
Part of the Oxford Respiratory Medicine Library series, this pocketbook aims to be a concise companion for all health care professionals who manage, or come across, patients with CF. The book covers all aspects of care, including both paediatric and adult-specific issues. The book will appeal to a wide variety of health professionals in respiratory medicine, paediatrics, and primary care.

Cystic Fibrosis (CF) is a multi-system disorder, requiring not just respiratory expertise but also management of nutrition, diabetes, musculoskeletal and psychosocial issues. This pocketbook is a concise companion for all health care professionals who manage patients with CF. The book covers all aspects of care, including both paediatric and adult-specific issues, and summarizes up-to-date literature in a concise and focussed style. There is an emphasis on the practical aspects of management with separate chapters covering the effects of CF in the lung, the microbiology of pulmonary CF, and management of exacerbations. Psychosocial aspects of CF care, end of life care and lung transplantation are also covered, and potential future therapies reviewed. This second edition has been extensively updated to reflect the UK CF Trust Standards of Care, treatment guidelines and Cochrane reviews. There are updates on emerging organisms; an expanded section on physiotherapy; and a new Pharmacopeia that covers all common CF medications.